MONTIOLI, Riccardo
 Distribuzione geografica
Continente #
NA - Nord America 3.907
EU - Europa 3.310
AS - Asia 2.844
SA - Sud America 386
AF - Africa 61
OC - Oceania 7
Continente sconosciuto - Info sul continente non disponibili 6
Totale 10.521
Nazione #
US - Stati Uniti d'America 3.828
RU - Federazione Russa 1.254
CN - Cina 1.083
SG - Singapore 977
GB - Regno Unito 757
IT - Italia 365
BR - Brasile 320
VN - Vietnam 294
HK - Hong Kong 216
SE - Svezia 180
DE - Germania 164
FR - Francia 161
IE - Irlanda 140
FI - Finlandia 119
KR - Corea 81
CA - Canada 47
UA - Ucraina 46
JP - Giappone 35
IN - India 30
PL - Polonia 27
BE - Belgio 21
IQ - Iraq 21
NL - Olanda 21
BD - Bangladesh 20
ID - Indonesia 20
AR - Argentina 19
MX - Messico 17
NG - Nigeria 17
EC - Ecuador 14
ZA - Sudafrica 14
ES - Italia 12
IL - Israele 11
TR - Turchia 11
AT - Austria 9
CL - Cile 8
UZ - Uzbekistan 8
AE - Emirati Arabi Uniti 7
AU - Australia 7
MA - Marocco 7
PK - Pakistan 7
VE - Venezuela 7
JO - Giordania 5
LT - Lituania 5
CO - Colombia 4
GR - Grecia 4
LV - Lettonia 4
MY - Malesia 4
PT - Portogallo 4
SA - Arabia Saudita 4
TN - Tunisia 4
UY - Uruguay 4
BG - Bulgaria 3
BO - Bolivia 3
CH - Svizzera 3
CR - Costa Rica 3
DO - Repubblica Dominicana 3
EU - Europa 3
PY - Paraguay 3
TG - Togo 3
A2 - ???statistics.table.value.countryCode.A2??? 2
AZ - Azerbaigian 2
BJ - Benin 2
DZ - Algeria 2
EG - Egitto 2
ET - Etiopia 2
JM - Giamaica 2
PE - Perù 2
RW - Ruanda 2
AM - Armenia 1
BA - Bosnia-Erzegovina 1
BH - Bahrain 1
BY - Bielorussia 1
CD - Congo 1
CG - Congo 1
CI - Costa d'Avorio 1
CU - Cuba 1
GF - Guiana Francese 1
GL - Groenlandia 1
GN - Guinea 1
GY - Guiana 1
HN - Honduras 1
HR - Croazia 1
IR - Iran 1
KE - Kenya 1
KG - Kirghizistan 1
KW - Kuwait 1
LU - Lussemburgo 1
LY - Libia 1
MD - Moldavia 1
MK - Macedonia 1
NO - Norvegia 1
NP - Nepal 1
PA - Panama 1
PR - Porto Rico 1
PS - Palestinian Territory 1
RO - Romania 1
RS - Serbia 1
SI - Slovenia 1
SK - Slovacchia (Repubblica Slovacca) 1
SV - El Salvador 1
Totale 10.518
Città #
Southend 665
Singapore 490
Dallas 470
Ashburn 433
Moscow 423
Chandler 384
San Jose 375
Jacksonville 255
Hong Kong 214
Ann Arbor 206
Beijing 191
Verona 190
Woodbridge 172
Dublin 140
Houston 127
The Dalles 120
Ho Chi Minh City 109
Jinan 86
Shenyang 77
New York 76
Wilmington 70
Hanoi 66
Los Angeles 66
Nanjing 63
Lawrence 58
Princeton 58
Redmond 43
Tianjin 42
Columbus 40
Hebei 39
Ningbo 33
São Paulo 33
Changsha 32
Helsinki 32
Munich 32
Tokyo 31
Buffalo 30
Santa Clara 27
Seattle 27
Zhengzhou 25
Nanchang 23
Seoul 23
Warsaw 23
Haikou 22
Hangzhou 22
Lanzhou 21
Brussels 20
Falls Church 20
Guangzhou 18
Redondo Beach 18
Orem 17
Redwood City 17
Taiyuan 17
Boston 16
Denver 16
Frankfurt am Main 16
Montreal 16
Council Bluffs 15
Jakarta 15
Taizhou 15
Toronto 15
Abuja 14
Chennai 14
Lancaster 13
London 13
Milan 13
Rome 13
San Francisco 13
Belo Horizonte 12
Dong Ket 12
Jiaxing 12
Kent 12
Rio de Janeiro 12
Boardman 11
Sindelfingen 11
Amsterdam 10
Brooklyn 10
Haiphong 10
Atlanta 9
Fuzhou 9
Johannesburg 9
Mexico City 9
Turku 9
Chicago 8
Da Nang 8
Dearborn 8
Elora 8
Perugia 8
Stockholm 8
Tashkent 8
Can Tho 7
Norwalk 7
Birmingham 6
Curitiba 6
Falkenstein 6
Kemerovo 6
Parma 6
Quito 6
Vienna 6
Amman 5
Totale 6.802
Nome #
Analisi cinetiche, spettrofotometriche e mutazionali di due enzimi PLP-dipendenti del fold type I. Meccanismi catalitici, processi di folding e dimerizzazione 300
Gly161 mutations associated with Primary Hyperoxaluria Type I induce the cytosolic aggregation and the intracellular degradation of the apo-form of alanine:glyoxylate aminotransferase 298
Dimerization and Folding Processes of Treponema denticola Cystalysin: The Role of Pyridoxal 5'-Phosphate 280
Holo-and apocystalysin from Treponema denticola: two different conformations 268
Biochemical and computational approaches to improve the clinical treatment of Dopa decarboxylase-related diseases: an overview 259
A comprehensive picture of the mutations associated with aromatic amino acid decarboxylase deficiency: from molecular mechanisms to therapy implications 228
Human wild-type alanine:glyoxylate aminotransferase and its naturally occurring G82E variant: functional properties and physiological implications 224
S250F variant associated with aromatic amino acid decarboxylase deficiency: molecular defects and intracellular rescue by pyridoxine 220
The novel R347g pathogenic mutation Of aromatic amino acid decarboxylase provides additional molecular insights into enzyme catalysis and deficiency 210
Effects of interface mutations on the dimerization of alanine glyoxylate aminotransferase and implications in the mistargeting of the pathogenic variants F152I and I244T 210
Pathogenic variants of human Aromatic L-Amino Acid Decarboxylase: evidences of misfolding in functionally active variants 206
Misfolding caused by the pathogenic mutation G47R on the minor allele of alanine:glyoxylate aminotransferase and chaperoning activity of pyridoxine 204
Biochemical analyses are instrumental in identifying the impact of mutations on holo and/or apo-forms and on the region(s) of alanine:glyoxylate aminotransferase variants associated with Primary Hyperoxaluria Type I. 201
Construction, purification and characterization of untagged human liver alanine-glyoxylate aminotransferase expressed in Escherichia coli 197
Caenorhabditis elegans AGXT-1 is a mitochondrial and temperature-adapted ortholog of peroxisomal human AGT1: New insights into between-species divergence in glyoxylate metabolism 196
An engineered folded PLP-bound monomer of Treponema denticola cystalysin reveals the effect of the dimeric structure on the catalytic properties of the enzyme 195
Human liver peroxisomal alanine:glyoxylate aminotransferase: Different stability under chemical stress of the major allele, the minor allele, and its pathogenic G170R variant. 191
Interaction of Human Dopa Decarboxylase with L-Dopa: Spectroscopic and Kinetic Studies as a Function of pH 189
Human liver peroxisomal alanine:glyoxylate aminotransferase: Characterization of the two allelic forms and their pathogenic variants. 183
Liver peroxisomal alanine:glyoxylate aminotransferase and the effects of mutations associated with Primary Hyperoxaluria Type I: An overview. 180
Cystalysin: an example of the catalytic versatility of pyridoxal 5'-phosphate dependent enzymes 178
New variants of AADC deficiency expand the knowledge of enzymatic phenotypes 175
The N-terminal extension is essential for the formation of the active dimeric structure of liver peroxisomal alanine:glyoxylate aminotransferase 174
Cysteine 180 Is a Redox Sensor Modulating the Activity of Human Pyridoxal 5'-Phosphate Histidine Decarboxylase 174
The Chaperoning Activity of Amino-oxyacetic Acid on Folding-Defective Variants of Human Alanine:Glyoxylate Aminotransferase Causing Primary Hyperoxaluria Type I 170
Molecular insight into the synergism between the minor allele of human liver peroxisomal alanine: Glyoxylate aminotransferase and the F152I mutation 169
Onconase Dimerization Through 3D Domain Swapping: Structural Investigations and Increase Of The Apoptotic Effect In Cancer Cells 169
Deciphering the fate of slan+ -monocytes in human tonsils by gene expression profiling 167
Tat-mediated delivery of human alanine:glyoxylate aminotransferase in a cellular model of Primary Hyperoxaluria Type I 164
S81 L and G170R mutations causing Primary Hyperoxaluria Type I in homozygosis and heterozygosis: an example of positive interallelic complementation. 162
Aromatic amino acid decarboxylase deficiency: the added value of biochemistry 162
Molecular insight into the synergism between the minor allele of human liver peroxisomal alanine: glyoxylate aminotransferase and the f152i mutation 161
Aromatic amino acid decarboxylase deficiency: Molecular and metabolic basis and therapeutic outlook 161
Oligomeric state and thermal stability of apo- and holo- human ornithine δ-aminotransferase 159
Dimerization of human angiogenin and of variants involved in neurodegenerative diseases 158
RNase A domain-swapped dimers produced through different methods: structure–catalytic properties and antitumor activity 156
Molecular defects of the glycine 41 variants of alanine glyoxylate aminotransferase associated with primary hyperoxaluria type I 154
Properties of RNase A monomer and dimers depend on the oligomerization pathway followed. 154
Deficit of human ornithine aminotransferase in gyrate atrophy: Molecular, cellular, and clinical aspects 154
Identification by Virtual Screening and In Vitro Testing of Human DOPA Decarboxylase Inhibitors 154
Molecular and cellular studies reveal folding defects of human ornithine aminotransferase variants associated with gyrate atrophy of the choroid and retina 151
The chaperone role of the pyridoxal 5′-phosphate and its implications for rare diseases involving B6-dependent enzymes 150
Natural and unnatural compounds rescue folding defects of human alanine:glyoxylate aminotransferase leading to Primary Hyperoxaluria Type I 149
Compound heterozygosis in AADC deficiency: A complex phenotype dissected through comparison among heterodimeric and homodimeric AADC proteins 149
Extensive deamidation of RNase A inhibits its oligomerization through 3D domain swapping 147
R180T variant of δ-ornithine aminotransferase associated with gyrate atrophy: biochemical, computational, X-RAY and NMR studies provide insight into its catalytic features 147
Radiation damage at the active site of human alanine:glyoxylate aminotransferase reveals that the cofactor position is finely tuned during catalysis 146
Molecular and cellular basis of ornithine δ-aminotransferase deficiency caused by the V332M mutation associated with gyrate atrophy of the choroid and retina 144
Biochemical and bioinformatic studies of mutations of residues at the monomer-monomer interface of human ornithine aminotransferase leading to gyrate atrophy of choroid and retina 143
A novel compound heterozygous genotype associated with aromatic amino acid decarboxylase deficiency: Clinical aspects and biochemical studies 143
Evidence for dimer/tetramer equilibrium in Trypanosoma brucei 6-phosphogluconate dehydrogenase 138
Insights into the mechanism of oxidative deamination catalyzed by Dopa decarboxylase 132
Probing the role of Tyr 64 of Treponema denticola cystalysin by site-directed mutagenesis and kinetic studies 129
Heterozygosis in aromatic amino acid decarboxylase deficiency: Evidence for a positive interallelic complementation between R347Q and R358H mutations 129
Molecular insights into the pathogenicity of variants associated with the aromatic amino acid decarboxylase deficiency. 128
Open conformation of human DOPA decarboxylase reveals the mechanism of PLP addition to Group II decarboxylases. 127
Biochemical investigation of pathogenic missense mutations of human 4-amino butyrate aminotransferase towards the understanding of the molecular pathogenesis of GABA transaminase deficiency 123
Parkinson's Disease: recent updates in the identification of human dopa decarboxylase inhibitors 123
Molecular insights into primary hyperoxaluria Type I pathogenesis. 119
Reactions of human liver peroxisomal alanine:glyoxylate aminotransferase with beta-chloro-L-alanine and L-cysteine: spectroscopic and kinetic analysis 115
Human RNase 1 can extensively oligomerize through 3D domain swapping thanks to the crucial contribution of its C-terminus 87
Spectrum of DDC variants causing aromatic l-amino acid decarboxylase (AADC) deficiency and pathogenicity interpretation using ACMG-AMP/ACGS recommendations 70
Current Insight into Human Ornithine Aminotransferase: A Review 13
Totale 10.616
Categoria #
all - tutte 32.295
article - articoli 29.817
book - libri 0
conference - conferenze 1.377
curatela - curatele 0
other - altro 635
patent - brevetti 0
selected - selezionate 0
volume - volumi 466
Totale 64.590


Totale Lug Ago Sett Ott Nov Dic Gen Feb Mar Apr Mag Giu
2020/202196 0 0 0 0 0 0 0 0 0 19 52 25
2021/2022716 51 242 116 29 25 11 10 36 22 21 34 119
2022/20231.071 76 131 87 191 93 243 20 53 122 6 29 20
2023/2024489 21 40 37 60 40 92 16 45 3 23 89 23
2024/20251.518 77 84 30 240 75 55 108 68 251 138 129 263
2025/20264.412 310 200 532 606 1.116 329 470 225 339 285 0 0
Totale 10.616