MONTIOLI, Riccardo
 Distribuzione geografica
Continente #
NA - Nord America 4.092
EU - Europa 3.333
AS - Asia 2.881
SA - Sud America 386
AF - Africa 61
OC - Oceania 7
Continente sconosciuto - Info sul continente non disponibili 6
Totale 10.766
Nazione #
US - Stati Uniti d'America 4.003
RU - Federazione Russa 1.254
CN - Cina 1.086
SG - Singapore 982
GB - Regno Unito 757
IT - Italia 381
BR - Brasile 320
VN - Vietnam 294
HK - Hong Kong 218
SE - Svezia 181
DE - Germania 164
FR - Francia 161
IE - Irlanda 141
FI - Finlandia 119
KR - Corea 81
CA - Canada 53
BD - Bangladesh 46
UA - Ucraina 46
JP - Giappone 35
IN - India 30
PL - Polonia 27
NL - Olanda 22
BE - Belgio 21
IQ - Iraq 21
ID - Indonesia 20
AR - Argentina 19
MX - Messico 18
NG - Nigeria 17
EC - Ecuador 14
ZA - Sudafrica 14
ES - Italia 12
TR - Turchia 12
IL - Israele 11
AT - Austria 9
CL - Cile 8
UZ - Uzbekistan 8
AE - Emirati Arabi Uniti 7
AU - Australia 7
MA - Marocco 7
PK - Pakistan 7
VE - Venezuela 7
LT - Lituania 6
JO - Giordania 5
CH - Svizzera 4
CO - Colombia 4
GR - Grecia 4
JM - Giamaica 4
LV - Lettonia 4
MY - Malesia 4
PT - Portogallo 4
SA - Arabia Saudita 4
TN - Tunisia 4
UY - Uruguay 4
BG - Bulgaria 3
BO - Bolivia 3
CR - Costa Rica 3
DO - Repubblica Dominicana 3
EU - Europa 3
PY - Paraguay 3
TG - Togo 3
A2 - ???statistics.table.value.countryCode.A2??? 2
AZ - Azerbaigian 2
BJ - Benin 2
DZ - Algeria 2
EG - Egitto 2
ET - Etiopia 2
MD - Moldavia 2
PE - Perù 2
RO - Romania 2
RW - Ruanda 2
SV - El Salvador 2
AM - Armenia 1
BA - Bosnia-Erzegovina 1
BH - Bahrain 1
BY - Bielorussia 1
CD - Congo 1
CG - Congo 1
CI - Costa d'Avorio 1
CU - Cuba 1
GF - Guiana Francese 1
GL - Groenlandia 1
GN - Guinea 1
GY - Guiana 1
HN - Honduras 1
HR - Croazia 1
IR - Iran 1
KE - Kenya 1
KG - Kirghizistan 1
KW - Kuwait 1
LU - Lussemburgo 1
LY - Libia 1
MK - Macedonia 1
NO - Norvegia 1
NP - Nepal 1
PA - Panama 1
PR - Porto Rico 1
PS - Palestinian Territory 1
RS - Serbia 1
SI - Slovenia 1
SK - Slovacchia (Repubblica Slovacca) 1
Totale 10.763
Città #
Southend 665
Singapore 493
Dallas 472
Ashburn 452
Moscow 423
San Jose 391
Chandler 384
Jacksonville 255
Hong Kong 216
Ann Arbor 206
Beijing 192
Verona 191
Woodbridge 172
Dublin 140
Houston 127
The Dalles 120
Ho Chi Minh City 109
Council Bluffs 93
Jinan 86
New York 84
Shenyang 77
Los Angeles 70
Wilmington 70
Hanoi 66
Nanjing 63
Lawrence 58
Princeton 58
Redmond 43
Tianjin 42
Columbus 40
Hebei 39
Buffalo 33
Ningbo 33
São Paulo 33
Changsha 32
Helsinki 32
Munich 32
Santa Clara 31
Tokyo 31
Seattle 27
Zhengzhou 25
Nanchang 23
Seoul 23
Warsaw 23
Haikou 22
Hangzhou 22
Lanzhou 21
Brussels 20
Falls Church 20
Denver 19
Guangzhou 18
Redondo Beach 18
Montreal 17
Orem 17
Redwood City 17
Taiyuan 17
Boston 16
Frankfurt am Main 16
Milan 16
Toronto 16
Jakarta 15
Taizhou 15
Abuja 14
Chennai 14
Rome 14
San Francisco 14
Lancaster 13
London 13
Belo Horizonte 12
Brooklyn 12
Dong Ket 12
Jiaxing 12
Kent 12
Rio de Janeiro 12
Boardman 11
Sindelfingen 11
Amsterdam 10
Haiphong 10
Mexico City 10
Atlanta 9
Fuzhou 9
Johannesburg 9
Turku 9
Chicago 8
Da Nang 8
Dearborn 8
Elora 8
Perugia 8
Stockholm 8
Tashkent 8
Can Tho 7
Norwalk 7
Birmingham 6
Curitiba 6
Falkenstein 6
Kemerovo 6
Parma 6
Quito 6
Shanghai 6
Vienna 6
Totale 6.957
Nome #
Analisi cinetiche, spettrofotometriche e mutazionali di due enzimi PLP-dipendenti del fold type I. Meccanismi catalitici, processi di folding e dimerizzazione 313
Gly161 mutations associated with Primary Hyperoxaluria Type I induce the cytosolic aggregation and the intracellular degradation of the apo-form of alanine:glyoxylate aminotransferase 303
Dimerization and Folding Processes of Treponema denticola Cystalysin: The Role of Pyridoxal 5'-Phosphate 283
Holo-and apocystalysin from Treponema denticola: two different conformations 270
Biochemical and computational approaches to improve the clinical treatment of Dopa decarboxylase-related diseases: an overview 262
A comprehensive picture of the mutations associated with aromatic amino acid decarboxylase deficiency: from molecular mechanisms to therapy implications 233
Human wild-type alanine:glyoxylate aminotransferase and its naturally occurring G82E variant: functional properties and physiological implications 227
S250F variant associated with aromatic amino acid decarboxylase deficiency: molecular defects and intracellular rescue by pyridoxine 225
Effects of interface mutations on the dimerization of alanine glyoxylate aminotransferase and implications in the mistargeting of the pathogenic variants F152I and I244T 215
The novel R347g pathogenic mutation Of aromatic amino acid decarboxylase provides additional molecular insights into enzyme catalysis and deficiency 212
Pathogenic variants of human Aromatic L-Amino Acid Decarboxylase: evidences of misfolding in functionally active variants 209
Misfolding caused by the pathogenic mutation G47R on the minor allele of alanine:glyoxylate aminotransferase and chaperoning activity of pyridoxine 206
Biochemical analyses are instrumental in identifying the impact of mutations on holo and/or apo-forms and on the region(s) of alanine:glyoxylate aminotransferase variants associated with Primary Hyperoxaluria Type I. 204
Construction, purification and characterization of untagged human liver alanine-glyoxylate aminotransferase expressed in Escherichia coli 202
An engineered folded PLP-bound monomer of Treponema denticola cystalysin reveals the effect of the dimeric structure on the catalytic properties of the enzyme 199
Caenorhabditis elegans AGXT-1 is a mitochondrial and temperature-adapted ortholog of peroxisomal human AGT1: New insights into between-species divergence in glyoxylate metabolism 199
Human liver peroxisomal alanine:glyoxylate aminotransferase: Different stability under chemical stress of the major allele, the minor allele, and its pathogenic G170R variant. 194
Interaction of Human Dopa Decarboxylase with L-Dopa: Spectroscopic and Kinetic Studies as a Function of pH 190
Oligomeric state and thermal stability of apo- and holo- human ornithine δ-aminotransferase 190
Human liver peroxisomal alanine:glyoxylate aminotransferase: Characterization of the two allelic forms and their pathogenic variants. 189
Cysteine 180 Is a Redox Sensor Modulating the Activity of Human Pyridoxal 5'-Phosphate Histidine Decarboxylase 182
Cystalysin: an example of the catalytic versatility of pyridoxal 5'-phosphate dependent enzymes 181
Liver peroxisomal alanine:glyoxylate aminotransferase and the effects of mutations associated with Primary Hyperoxaluria Type I: An overview. 181
New variants of AADC deficiency expand the knowledge of enzymatic phenotypes 181
The N-terminal extension is essential for the formation of the active dimeric structure of liver peroxisomal alanine:glyoxylate aminotransferase 178
Molecular insight into the synergism between the minor allele of human liver peroxisomal alanine: Glyoxylate aminotransferase and the F152I mutation 173
Onconase Dimerization Through 3D Domain Swapping: Structural Investigations and Increase Of The Apoptotic Effect In Cancer Cells 173
Deciphering the fate of slan+ -monocytes in human tonsils by gene expression profiling 172
The Chaperoning Activity of Amino-oxyacetic Acid on Folding-Defective Variants of Human Alanine:Glyoxylate Aminotransferase Causing Primary Hyperoxaluria Type I 171
S81 L and G170R mutations causing Primary Hyperoxaluria Type I in homozygosis and heterozygosis: an example of positive interallelic complementation. 168
Tat-mediated delivery of human alanine:glyoxylate aminotransferase in a cellular model of Primary Hyperoxaluria Type I 165
Dimerization of human angiogenin and of variants involved in neurodegenerative diseases 163
Aromatic amino acid decarboxylase deficiency: Molecular and metabolic basis and therapeutic outlook 162
Aromatic amino acid decarboxylase deficiency: the added value of biochemistry 162
Molecular insight into the synergism between the minor allele of human liver peroxisomal alanine: glyoxylate aminotransferase and the f152i mutation 161
RNase A domain-swapped dimers produced through different methods: structure–catalytic properties and antitumor activity 160
Molecular defects of the glycine 41 variants of alanine glyoxylate aminotransferase associated with primary hyperoxaluria type I 157
Properties of RNase A monomer and dimers depend on the oligomerization pathway followed. 157
Natural and unnatural compounds rescue folding defects of human alanine:glyoxylate aminotransferase leading to Primary Hyperoxaluria Type I 156
Deficit of human ornithine aminotransferase in gyrate atrophy: Molecular, cellular, and clinical aspects 155
Identification by Virtual Screening and In Vitro Testing of Human DOPA Decarboxylase Inhibitors 155
Compound heterozygosis in AADC deficiency: A complex phenotype dissected through comparison among heterodimeric and homodimeric AADC proteins 154
Molecular and cellular studies reveal folding defects of human ornithine aminotransferase variants associated with gyrate atrophy of the choroid and retina 153
The chaperone role of the pyridoxal 5′-phosphate and its implications for rare diseases involving B6-dependent enzymes 151
Radiation damage at the active site of human alanine:glyoxylate aminotransferase reveals that the cofactor position is finely tuned during catalysis 150
Extensive deamidation of RNase A inhibits its oligomerization through 3D domain swapping 149
R180T variant of δ-ornithine aminotransferase associated with gyrate atrophy: biochemical, computational, X-RAY and NMR studies provide insight into its catalytic features 149
Molecular and cellular basis of ornithine δ-aminotransferase deficiency caused by the V332M mutation associated with gyrate atrophy of the choroid and retina 148
Biochemical and bioinformatic studies of mutations of residues at the monomer-monomer interface of human ornithine aminotransferase leading to gyrate atrophy of choroid and retina 143
A novel compound heterozygous genotype associated with aromatic amino acid decarboxylase deficiency: Clinical aspects and biochemical studies 143
Evidence for dimer/tetramer equilibrium in Trypanosoma brucei 6-phosphogluconate dehydrogenase 141
Heterozygosis in aromatic amino acid decarboxylase deficiency: Evidence for a positive interallelic complementation between R347Q and R358H mutations 137
Insights into the mechanism of oxidative deamination catalyzed by Dopa decarboxylase 135
Open conformation of human DOPA decarboxylase reveals the mechanism of PLP addition to Group II decarboxylases. 131
Probing the role of Tyr 64 of Treponema denticola cystalysin by site-directed mutagenesis and kinetic studies 130
Molecular insights into the pathogenicity of variants associated with the aromatic amino acid decarboxylase deficiency. 128
Biochemical investigation of pathogenic missense mutations of human 4-amino butyrate aminotransferase towards the understanding of the molecular pathogenesis of GABA transaminase deficiency 125
Molecular insights into primary hyperoxaluria Type I pathogenesis. 125
Parkinson's Disease: recent updates in the identification of human dopa decarboxylase inhibitors 125
Reactions of human liver peroxisomal alanine:glyoxylate aminotransferase with beta-chloro-L-alanine and L-cysteine: spectroscopic and kinetic analysis 116
Human RNase 1 can extensively oligomerize through 3D domain swapping thanks to the crucial contribution of its C-terminus 97
Spectrum of DDC variants causing aromatic l-amino acid decarboxylase (AADC) deficiency and pathogenicity interpretation using ACMG-AMP/ACGS recommendations 77
Current Insight into Human Ornithine Aminotransferase: A Review 16
Totale 10.861
Categoria #
all - tutte 34.106
article - articoli 31.497
book - libri 0
conference - conferenze 1.448
curatela - curatele 0
other - altro 668
patent - brevetti 0
selected - selezionate 0
volume - volumi 493
Totale 68.212


Totale Lug Ago Sett Ott Nov Dic Gen Feb Mar Apr Mag Giu
2020/202125 0 0 0 0 0 0 0 0 0 0 0 25
2021/2022716 51 242 116 29 25 11 10 36 22 21 34 119
2022/20231.071 76 131 87 191 93 243 20 53 122 6 29 20
2023/2024489 21 40 37 60 40 92 16 45 3 23 89 23
2024/20251.518 77 84 30 240 75 55 108 68 251 138 129 263
2025/20264.657 310 200 532 606 1.116 329 470 225 339 296 98 136
Totale 10.861