CATALOGO DEI PRODOTTI DELLA RICERCA

MONTIOLI, Riccardo
 Distribuzione geografica
Salva come PNG Salva come JPEG
Continente #
EU - Europa 3.185
NA - Nord America 3.169
AS - Asia 2.417
SA - Sud America 353
AF - Africa 38
Continente sconosciuto - Info sul continente non disponibili 6
OC - Oceania 5
Totale 9.173
Salva come PNG Salva come JPEG
Nazione #
US - Stati Uniti d'America 3.103
RU - Federazione Russa 1.254
CN - Cina 1.004
SG - Singapore 845
GB - Regno Unito 747
BR - Brasile 307
IT - Italia 293
HK - Hong Kong 205
SE - Svezia 178
VN - Vietnam 168
DE - Germania 156
FR - Francia 153
IE - Irlanda 139
FI - Finlandia 117
KR - Corea 51
UA - Ucraina 43
CA - Canada 41
JP - Giappone 31
PL - Polonia 24
BE - Belgio 21
ID - Indonesia 19
IN - India 18
BD - Bangladesh 16
NL - Olanda 15
AR - Argentina 13
IQ - Iraq 13
MX - Messico 13
EC - Ecuador 12
ES - Italia 12
ZA - Sudafrica 12
IL - Israele 11
TR - Turchia 8
AT - Austria 7
CL - Cile 7
AE - Emirati Arabi Uniti 6
MA - Marocco 6
AU - Australia 5
LT - Lituania 4
LV - Lettonia 4
UZ - Uzbekistan 4
VE - Venezuela 4
BG - Bulgaria 3
CO - Colombia 3
DO - Repubblica Dominicana 3
EU - Europa 3
JO - Giordania 3
PK - Pakistan 3
PT - Portogallo 3
SA - Arabia Saudita 3
TG - Togo 3
A2 - ???statistics.table.value.countryCode.A2??? 2
BJ - Benin 2
CH - Svizzera 2
DZ - Algeria 2
ET - Etiopia 2
GR - Grecia 2
JM - Giamaica 2
PY - Paraguay 2
RW - Ruanda 2
TN - Tunisia 2
AM - Armenia 1
AZ - Azerbaigian 1
BA - Bosnia-Erzegovina 1
BH - Bahrain 1
BO - Bolivia 1
BY - Bielorussia 1
CD - Congo 1
CG - Congo 1
CR - Costa Rica 1
CU - Cuba 1
EG - Egitto 1
GF - Guiana Francese 1
GL - Groenlandia 1
GN - Guinea 1
GY - Guiana 1
HN - Honduras 1
IR - Iran 1
KE - Kenya 1
KG - Kirghizistan 1
LU - Lussemburgo 1
LY - Libia 1
MD - Moldavia 1
MK - Macedonia 1
MY - Malesia 1
NG - Nigeria 1
NP - Nepal 1
PA - Panama 1
PE - Perù 1
PS - Palestinian Territory 1
RO - Romania 1
SI - Slovenia 1
SK - Slovacchia (Repubblica Slovacca) 1
SV - El Salvador 1
TH - Thailandia 1
TT - Trinidad e Tobago 1
UY - Uruguay 1
XK - ???statistics.table.value.countryCode.XK??? 1
Totale 9.173
Salva come PNG Salva come JPEG
Città #
Southend 665
Dallas 470
Moscow 423
Chandler 384
Singapore 384
Jacksonville 255
Ashburn 224
Ann Arbor 206
Hong Kong 203
Beijing 190
Woodbridge 172
Dublin 139
Verona 128
Houston 126
The Dalles 94
Jinan 86
Shenyang 77
New York 74
Wilmington 70
Nanjing 63
Ho Chi Minh City 59
Lawrence 58
Princeton 58
Los Angeles 57
Redmond 43
Tianjin 41
Columbus 40
Hebei 39
Hanoi 33
Ningbo 33
Changsha 32
Munich 32
São Paulo 32
Helsinki 30
Buffalo 29
Tokyo 28
Seattle 27
Zhengzhou 24
Nanchang 23
Haikou 22
Seoul 22
Hangzhou 21
Lanzhou 21
Santa Clara 21
Warsaw 21
Brussels 20
Falls Church 20
Redondo Beach 18
Guangzhou 17
Redwood City 17
Taiyuan 17
Boston 16
Jakarta 15
Taizhou 15
Toronto 14
Denver 13
Lancaster 13
Montreal 13
San Francisco 13
Dong Ket 12
Jiaxing 12
Kent 12
Milan 12
Rio de Janeiro 12
Rome 12
Belo Horizonte 11
Boardman 11
London 11
Sindelfingen 11
Brooklyn 10
Council Bluffs 10
Frankfurt am Main 10
Orem 10
Fuzhou 9
Turku 9
Dearborn 8
Elora 8
Johannesburg 8
Perugia 8
Amsterdam 7
Chennai 7
Chicago 7
Haiphong 7
Mexico City 7
Norwalk 7
Stockholm 7
Birmingham 6
Curitiba 6
Falkenstein 6
Kemerovo 6
Parma 6
Quito 6
Atlanta 5
Betim 5
Manaus 5
Phoenix 5
Auburn Hills 4
Brasília 4
Cagliari 4
Can Tho 4
Totale 5.827
Salva come PNG Salva come JPEG
Nome #
Analisi cinetiche, spettrofotometriche e mutazionali di due enzimi PLP-dipendenti del fold type I. Meccanismi catalitici, processi di folding e dimerizzazione 280
Gly161 mutations associated with Primary Hyperoxaluria Type I induce the cytosolic aggregation and the intracellular degradation of the apo-form of alanine:glyoxylate aminotransferase 263
Dimerization and Folding Processes of Treponema denticola Cystalysin: The Role of Pyridoxal 5'-Phosphate 242
Biochemical and computational approaches to improve the clinical treatment of Dopa decarboxylase-related diseases: an overview 241
Holo-and apocystalysin from Treponema denticola: two different conformations 238
A comprehensive picture of the mutations associated with aromatic amino acid decarboxylase deficiency: from molecular mechanisms to therapy implications 203
The novel R347g pathogenic mutation Of aromatic amino acid decarboxylase provides additional molecular insights into enzyme catalysis and deficiency 196
S250F variant associated with aromatic amino acid decarboxylase deficiency: molecular defects and intracellular rescue by pyridoxine 190
Effects of interface mutations on the dimerization of alanine glyoxylate aminotransferase and implications in the mistargeting of the pathogenic variants F152I and I244T 185
Misfolding caused by the pathogenic mutation G47R on the minor allele of alanine:glyoxylate aminotransferase and chaperoning activity of pyridoxine 185
Human wild-type alanine:glyoxylate aminotransferase and its naturally occurring G82E variant: functional properties and physiological implications 183
Biochemical analyses are instrumental in identifying the impact of mutations on holo and/or apo-forms and on the region(s) of alanine:glyoxylate aminotransferase variants associated with Primary Hyperoxaluria Type I. 179
Construction, purification and characterization of untagged human liver alanine-glyoxylate aminotransferase expressed in Escherichia coli 174
Pathogenic variants of human Aromatic L-Amino Acid Decarboxylase: evidences of misfolding in functionally active variants 172
Interaction of Human Dopa Decarboxylase with L-Dopa: Spectroscopic and Kinetic Studies as a Function of pH 171
An engineered folded PLP-bound monomer of Treponema denticola cystalysin reveals the effect of the dimeric structure on the catalytic properties of the enzyme 170
Caenorhabditis elegans AGXT-1 is a mitochondrial and temperature-adapted ortholog of peroxisomal human AGT1: New insights into between-species divergence in glyoxylate metabolism 169
Human liver peroxisomal alanine:glyoxylate aminotransferase: Different stability under chemical stress of the major allele, the minor allele, and its pathogenic G170R variant. 167
Human liver peroxisomal alanine:glyoxylate aminotransferase: Characterization of the two allelic forms and their pathogenic variants. 165
Cystalysin: an example of the catalytic versatility of pyridoxal 5'-phosphate dependent enzymes 159
Liver peroxisomal alanine:glyoxylate aminotransferase and the effects of mutations associated with Primary Hyperoxaluria Type I: An overview. 159
Tat-mediated delivery of human alanine:glyoxylate aminotransferase in a cellular model of Primary Hyperoxaluria Type I 152
The Chaperoning Activity of Amino-oxyacetic Acid on Folding-Defective Variants of Human Alanine:Glyoxylate Aminotransferase Causing Primary Hyperoxaluria Type I 151
Onconase Dimerization Through 3D Domain Swapping: Structural Investigations and Increase Of The Apoptotic Effect In Cancer Cells 149
Molecular insight into the synergism between the minor allele of human liver peroxisomal alanine: glyoxylate aminotransferase and the f152i mutation 149
Molecular insight into the synergism between the minor allele of human liver peroxisomal alanine: Glyoxylate aminotransferase and the F152I mutation 148
New variants of AADC deficiency expand the knowledge of enzymatic phenotypes 148
Cysteine 180 Is a Redox Sensor Modulating the Activity of Human Pyridoxal 5'-Phosphate Histidine Decarboxylase 147
Molecular defects of the glycine 41 variants of alanine glyoxylate aminotransferase associated with primary hyperoxaluria type I 143
The N-terminal extension is essential for the formation of the active dimeric structure of liver peroxisomal alanine:glyoxylate aminotransferase 142
S81 L and G170R mutations causing Primary Hyperoxaluria Type I in homozygosis and heterozygosis: an example of positive interallelic complementation. 141
Aromatic amino acid decarboxylase deficiency: the added value of biochemistry 140
Aromatic amino acid decarboxylase deficiency: Molecular and metabolic basis and therapeutic outlook 139
Identification by Virtual Screening and In Vitro Testing of Human DOPA Decarboxylase Inhibitors 139
Properties of RNase A monomer and dimers depend on the oligomerization pathway followed. 138
Deciphering the fate of slan+ -monocytes in human tonsils by gene expression profiling 138
RNase A domain-swapped dimers produced through different methods: structure–catalytic properties and antitumor activity 138
Compound heterozygosis in AADC deficiency: A complex phenotype dissected through comparison among heterodimeric and homodimeric AADC proteins 137
Radiation damage at the active site of human alanine:glyoxylate aminotransferase reveals that the cofactor position is finely tuned during catalysis 136
Deficit of human ornithine aminotransferase in gyrate atrophy: Molecular, cellular, and clinical aspects 135
Dimerization of human angiogenin and of variants involved in neurodegenerative diseases 132
Extensive deamidation of RNase A inhibits its oligomerization through 3D domain swapping 130
Natural and unnatural compounds rescue folding defects of human alanine:glyoxylate aminotransferase leading to Primary Hyperoxaluria Type I 128
Molecular and cellular studies reveal folding defects of human ornithine aminotransferase variants associated with gyrate atrophy of the choroid and retina 128
Evidence for dimer/tetramer equilibrium in Trypanosoma brucei 6-phosphogluconate dehydrogenase 126
Oligomeric state and thermal stability of apo- and holo- human ornithine δ-aminotransferase 126
The chaperone role of the pyridoxal 5′-phosphate and its implications for rare diseases involving B6-dependent enzymes 125
A novel compound heterozygous genotype associated with aromatic amino acid decarboxylase deficiency: Clinical aspects and biochemical studies 121
R180T variant of δ-ornithine aminotransferase associated with gyrate atrophy: biochemical, computational, X-RAY and NMR studies provide insight into its catalytic features 119
Insights into the mechanism of oxidative deamination catalyzed by Dopa decarboxylase 118
Probing the role of Tyr 64 of Treponema denticola cystalysin by site-directed mutagenesis and kinetic studies 117
Open conformation of human DOPA decarboxylase reveals the mechanism of PLP addition to Group II decarboxylases. 113
Molecular insights into the pathogenicity of variants associated with the aromatic amino acid decarboxylase deficiency. 112
Heterozygosis in aromatic amino acid decarboxylase deficiency: Evidence for a positive interallelic complementation between R347Q and R358H mutations 112
Molecular and cellular basis of ornithine δ-aminotransferase deficiency caused by the V332M mutation associated with gyrate atrophy of the choroid and retina 112
Parkinson's Disease: recent updates in the identification of human dopa decarboxylase inhibitors 107
Biochemical and bioinformatic studies of mutations of residues at the monomer-monomer interface of human ornithine aminotransferase leading to gyrate atrophy of choroid and retina 106
Reactions of human liver peroxisomal alanine:glyoxylate aminotransferase with beta-chloro-L-alanine and L-cysteine: spectroscopic and kinetic analysis 105
Biochemical investigation of pathogenic missense mutations of human 4-amino butyrate aminotransferase towards the understanding of the molecular pathogenesis of GABA transaminase deficiency 103
Molecular insights into primary hyperoxaluria Type I pathogenesis. 103
Human RNase 1 can extensively oligomerize through 3D domain swapping thanks to the crucial contribution of its C-terminus 67
Spectrum of DDC variants causing aromatic l-amino acid decarboxylase (AADC) deficiency and pathogenicity interpretation using ACMG-AMP/ACGS recommendations 56
Totale 9.267
Salva come PNG Salva come JPEG
Categoria #
all - tutte 29.700
article - articoli 27.394
book - libri 0
conference - conferenze 1.273
curatela - curatele 0
other - altro 598
patent - brevetti 0
selected - selezionate 0
volume - volumi 435
Totale 59.400
Salva come PNG Salva come JPEG


Totale Lug Ago Sett Ott Nov Dic Gen Feb Mar Apr Mag Giu
2020/2021216 0 0 0 0 0 50 9 37 24 19 52 25
2021/2022716 51 242 116 29 25 11 10 36 22 21 34 119
2022/20231.071 76 131 87 191 93 243 20 53 122 6 29 20
2023/2024489 21 40 37 60 40 92 16 45 3 23 89 23
2024/20251.518 77 84 30 240 75 55 108 68 251 138 129 263
2025/20263.063 310 200 532 606 1.116 299 0 0 0 0 0 0
Totale 9.267