CATALOGO DEI PRODOTTI DELLA RICERCA

MONTIOLI, Riccardo
 Distribuzione geografica
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Continente #
NA - Nord America 2.757
EU - Europa 2.044
AS - Asia 1.878
SA - Sud America 290
AF - Africa 31
Continente sconosciuto - Info sul continente non disponibili 6
OC - Oceania 5
Totale 7.011
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Nazione #
US - Stati Uniti d'America 2.705
CN - Cina 878
GB - Regno Unito 739
SG - Singapore 600
IT - Italia 286
BR - Brasile 266
HK - Hong Kong 197
SE - Svezia 175
RU - Federazione Russa 162
FR - Francia 153
DE - Germania 151
IE - Irlanda 139
FI - Finlandia 115
VN - Vietnam 64
UA - Ucraina 42
KR - Corea 39
CA - Canada 34
JP - Giappone 22
BE - Belgio 21
PL - Polonia 17
ID - Indonesia 12
ZA - Sudafrica 11
IQ - Iraq 10
NL - Olanda 10
IN - India 9
BD - Bangladesh 8
EC - Ecuador 8
IL - Israele 8
MX - Messico 7
TR - Turchia 7
AE - Emirati Arabi Uniti 6
AT - Austria 6
AU - Australia 5
ES - Italia 5
CL - Cile 4
LV - Lettonia 4
MA - Marocco 4
AR - Argentina 3
BG - Bulgaria 3
CO - Colombia 3
EU - Europa 3
LT - Lituania 3
PK - Pakistan 3
PT - Portogallo 3
TG - Togo 3
A2 - ???statistics.table.value.countryCode.A2??? 2
CH - Svizzera 2
DO - Repubblica Dominicana 2
DZ - Algeria 2
GR - Grecia 2
JM - Giamaica 2
JO - Giordania 2
RW - Ruanda 2
SA - Arabia Saudita 2
TN - Tunisia 2
UZ - Uzbekistan 2
AM - Armenia 1
AZ - Azerbaigian 1
BA - Bosnia-Erzegovina 1
BH - Bahrain 1
BO - Bolivia 1
CD - Congo 1
CG - Congo 1
CR - Costa Rica 1
CU - Cuba 1
EG - Egitto 1
ET - Etiopia 1
GF - Guiana Francese 1
GL - Groenlandia 1
GN - Guinea 1
GY - Guiana 1
HN - Honduras 1
IR - Iran 1
KG - Kirghizistan 1
LU - Lussemburgo 1
LY - Libia 1
MK - Macedonia 1
MY - Malesia 1
NG - Nigeria 1
NP - Nepal 1
PA - Panama 1
PS - Palestinian Territory 1
PY - Paraguay 1
RO - Romania 1
SI - Slovenia 1
SK - Slovacchia (Repubblica Slovacca) 1
SV - El Salvador 1
TH - Thailandia 1
TT - Trinidad e Tobago 1
UY - Uruguay 1
VE - Venezuela 1
XK - ???statistics.table.value.countryCode.XK??? 1
Totale 7.011
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Città #
Southend 665
Chandler 384
Dallas 371
Jacksonville 255
Singapore 240
Ann Arbor 206
Hong Kong 195
Woodbridge 172
Beijing 156
Dublin 139
Verona 128
Houston 120
Ashburn 117
Jinan 86
Shenyang 76
Wilmington 70
Nanjing 63
New York 63
Lawrence 58
Princeton 58
The Dalles 52
Redmond 43
Columbus 40
Hebei 39
Los Angeles 33
Ningbo 33
Munich 32
Changsha 31
Helsinki 30
Tianjin 30
Seattle 25
São Paulo 24
Ho Chi Minh City 23
Nanchang 23
Zhengzhou 23
Haikou 22
Lanzhou 21
Brussels 20
Falls Church 20
Seoul 20
Hangzhou 19
Tokyo 19
Redwood City 17
Taiyuan 17
Guangzhou 15
Santa Clara 15
Taizhou 15
Warsaw 15
Buffalo 14
Lancaster 13
San Francisco 13
Dong Ket 12
Jiaxing 12
Kent 12
Rio de Janeiro 12
Toronto 12
Belo Horizonte 11
Boardman 11
Boston 11
Jakarta 11
Milan 11
Rome 11
Sindelfingen 11
Council Bluffs 10
Frankfurt am Main 10
Brooklyn 9
Fuzhou 9
Montreal 9
Turku 9
Dearborn 8
Elora 8
Hanoi 8
Johannesburg 8
London 8
Perugia 8
Redondo Beach 8
Norwalk 7
Birmingham 6
Chicago 6
Kemerovo 6
Parma 6
Curitiba 5
Manaus 5
Auburn Hills 4
Betim 4
Cagliari 4
Dongguan 4
Fairfield 4
Mexico City 4
Padova 4
Phoenix 4
Qingdao 4
Quito 4
Shanghai 4
Stockholm 4
Vienna 4
Washington 4
Atlanta 3
Brasília 3
Brescia 3
Totale 4.733
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Nome #
Analisi cinetiche, spettrofotometriche e mutazionali di due enzimi PLP-dipendenti del fold type I. Meccanismi catalitici, processi di folding e dimerizzazione 240
Gly161 mutations associated with Primary Hyperoxaluria Type I induce the cytosolic aggregation and the intracellular degradation of the apo-form of alanine:glyoxylate aminotransferase 215
Dimerization and Folding Processes of Treponema denticola Cystalysin: The Role of Pyridoxal 5'-Phosphate 192
Biochemical and computational approaches to improve the clinical treatment of Dopa decarboxylase-related diseases: an overview 191
Holo-and apocystalysin from Treponema denticola: two different conformations 189
Human wild-type alanine:glyoxylate aminotransferase and its naturally occurring G82E variant: functional properties and physiological implications 160
S250F variant associated with aromatic amino acid decarboxylase deficiency: molecular defects and intracellular rescue by pyridoxine 143
A comprehensive picture of the mutations associated with aromatic amino acid decarboxylase deficiency: from molecular mechanisms to therapy implications 142
The novel R347g pathogenic mutation Of aromatic amino acid decarboxylase provides additional molecular insights into enzyme catalysis and deficiency 141
Construction, purification and characterization of untagged human liver alanine-glyoxylate aminotransferase expressed in Escherichia coli 140
Interaction of Human Dopa Decarboxylase with L-Dopa: Spectroscopic and Kinetic Studies as a Function of pH 136
Biochemical analyses are instrumental in identifying the impact of mutations on holo and/or apo-forms and on the region(s) of alanine:glyoxylate aminotransferase variants associated with Primary Hyperoxaluria Type I. 134
Effects of interface mutations on the dimerization of alanine glyoxylate aminotransferase and implications in the mistargeting of the pathogenic variants F152I and I244T 133
Human liver peroxisomal alanine:glyoxylate aminotransferase: Characterization of the two allelic forms and their pathogenic variants. 130
Caenorhabditis elegans AGXT-1 is a mitochondrial and temperature-adapted ortholog of peroxisomal human AGT1: New insights into between-species divergence in glyoxylate metabolism 130
Human liver peroxisomal alanine:glyoxylate aminotransferase: Different stability under chemical stress of the major allele, the minor allele, and its pathogenic G170R variant. 129
Pathogenic variants of human Aromatic L-Amino Acid Decarboxylase: evidences of misfolding in functionally active variants 128
Misfolding caused by the pathogenic mutation G47R on the minor allele of alanine:glyoxylate aminotransferase and chaperoning activity of pyridoxine 128
An engineered folded PLP-bound monomer of Treponema denticola cystalysin reveals the effect of the dimeric structure on the catalytic properties of the enzyme 123
Liver peroxisomal alanine:glyoxylate aminotransferase and the effects of mutations associated with Primary Hyperoxaluria Type I: An overview. 123
Cystalysin: an example of the catalytic versatility of pyridoxal 5'-phosphate dependent enzymes 122
Tat-mediated delivery of human alanine:glyoxylate aminotransferase in a cellular model of Primary Hyperoxaluria Type I 122
Identification by Virtual Screening and In Vitro Testing of Human DOPA Decarboxylase Inhibitors 122
Molecular insight into the synergism between the minor allele of human liver peroxisomal alanine: glyoxylate aminotransferase and the f152i mutation 119
Molecular insight into the synergism between the minor allele of human liver peroxisomal alanine: Glyoxylate aminotransferase and the F152I mutation 118
Molecular defects of the glycine 41 variants of alanine glyoxylate aminotransferase associated with primary hyperoxaluria type I 117
The N-terminal extension is essential for the formation of the active dimeric structure of liver peroxisomal alanine:glyoxylate aminotransferase 117
Radiation damage at the active site of human alanine:glyoxylate aminotransferase reveals that the cofactor position is finely tuned during catalysis 117
The Chaperoning Activity of Amino-oxyacetic Acid on Folding-Defective Variants of Human Alanine:Glyoxylate Aminotransferase Causing Primary Hyperoxaluria Type I 113
Evidence for dimer/tetramer equilibrium in Trypanosoma brucei 6-phosphogluconate dehydrogenase 110
The chaperone role of the pyridoxal 5′-phosphate and its implications for rare diseases involving B6-dependent enzymes 109
New variants of AADC deficiency expand the knowledge of enzymatic phenotypes 109
Insights into the mechanism of oxidative deamination catalyzed by Dopa decarboxylase 108
Onconase Dimerization Through 3D Domain Swapping: Structural Investigations and Increase Of The Apoptotic Effect In Cancer Cells 108
Oligomeric state and thermal stability of apo- and holo- human ornithine δ-aminotransferase 107
Aromatic amino acid decarboxylase deficiency: the added value of biochemistry 105
S81 L and G170R mutations causing Primary Hyperoxaluria Type I in homozygosis and heterozygosis: an example of positive interallelic complementation. 104
Cysteine 180 Is a Redox Sensor Modulating the Activity of Human Pyridoxal 5'-Phosphate Histidine Decarboxylase 104
Aromatic amino acid decarboxylase deficiency: Molecular and metabolic basis and therapeutic outlook 102
Molecular and cellular studies reveal folding defects of human ornithine aminotransferase variants associated with gyrate atrophy of the choroid and retina 102
Probing the role of Tyr 64 of Treponema denticola cystalysin by site-directed mutagenesis and kinetic studies 100
Extensive deamidation of RNase A inhibits its oligomerization through 3D domain swapping 100
Deficit of human ornithine aminotransferase in gyrate atrophy: Molecular, cellular, and clinical aspects 99
Open conformation of human DOPA decarboxylase reveals the mechanism of PLP addition to Group II decarboxylases. 97
Properties of RNase A monomer and dimers depend on the oligomerization pathway followed. 97
RNase A domain-swapped dimers produced through different methods: structure–catalytic properties and antitumor activity 97
Compound heterozygosis in AADC deficiency: A complex phenotype dissected through comparison among heterodimeric and homodimeric AADC proteins 97
Deciphering the fate of slan+ -monocytes in human tonsils by gene expression profiling 96
Molecular insights into the pathogenicity of variants associated with the aromatic amino acid decarboxylase deficiency. 94
Natural and unnatural compounds rescue folding defects of human alanine:glyoxylate aminotransferase leading to Primary Hyperoxaluria Type I 93
Heterozygosis in aromatic amino acid decarboxylase deficiency: Evidence for a positive interallelic complementation between R347Q and R358H mutations 92
Dimerization of human angiogenin and of variants involved in neurodegenerative diseases 91
Reactions of human liver peroxisomal alanine:glyoxylate aminotransferase with beta-chloro-L-alanine and L-cysteine: spectroscopic and kinetic analysis 90
R180T variant of δ-ornithine aminotransferase associated with gyrate atrophy: biochemical, computational, X-RAY and NMR studies provide insight into its catalytic features 90
Molecular and cellular basis of ornithine δ-aminotransferase deficiency caused by the V332M mutation associated with gyrate atrophy of the choroid and retina 89
Molecular insights into primary hyperoxaluria Type I pathogenesis. 87
Parkinson's Disease: recent updates in the identification of human dopa decarboxylase inhibitors 83
A novel compound heterozygous genotype associated with aromatic amino acid decarboxylase deficiency: Clinical aspects and biochemical studies 74
Biochemical and bioinformatic studies of mutations of residues at the monomer-monomer interface of human ornithine aminotransferase leading to gyrate atrophy of choroid and retina 60
Spectrum of DDC variants causing aromatic l-amino acid decarboxylase (AADC) deficiency and pathogenicity interpretation using ACMG-AMP/ACGS recommendations 39
Human RNase 1 can extensively oligomerize through 3D domain swapping thanks to the crucial contribution of its C-terminus 34
Biochemical investigation of pathogenic missense mutations of human 4-amino butyrate aminotransferase towards the understanding of the molecular pathogenesis of GABA transaminase deficiency 24
Totale 7.105
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Categoria #
all - tutte 25.268
article - articoli 23.295
book - libri 0
conference - conferenze 1.072
curatela - curatele 0
other - altro 533
patent - brevetti 0
selected - selezionate 0
volume - volumi 368
Totale 50.536
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Totale Lug Ago Sett Ott Nov Dic Gen Feb Mar Apr Mag Giu
2020/2021399 0 0 27 77 79 50 9 37 24 19 52 25
2021/2022716 51 242 116 29 25 11 10 36 22 21 34 119
2022/20231.071 76 131 87 191 93 243 20 53 122 6 29 20
2023/2024489 21 40 37 60 40 92 16 45 3 23 89 23
2024/20251.518 77 84 30 240 75 55 108 68 251 138 129 263
2025/2026901 310 200 391 0 0 0 0 0 0 0 0 0
Totale 7.105