MONTIOLI, Riccardo
 Distribuzione geografica
Continente #
NA - Nord America 3.069
EU - Europa 3.054
AS - Asia 2.225
SA - Sud America 344
AF - Africa 35
Continente sconosciuto - Info sul continente non disponibili 6
OC - Oceania 5
Totale 8.738
Nazione #
US - Stati Uniti d'America 3.004
RU - Federazione Russa 1.128
CN - Cina 992
GB - Regno Unito 747
SG - Singapore 703
BR - Brasile 303
IT - Italia 293
HK - Hong Kong 203
SE - Svezia 176
DE - Germania 156
FR - Francia 153
VN - Vietnam 147
IE - Irlanda 139
FI - Finlandia 117
KR - Corea 49
UA - Ucraina 43
CA - Canada 40
JP - Giappone 30
PL - Polonia 24
BE - Belgio 21
ID - Indonesia 19
IN - India 17
NL - Olanda 15
MX - Messico 13
AR - Argentina 12
EC - Ecuador 12
ES - Italia 12
IQ - Iraq 12
ZA - Sudafrica 12
IL - Israele 11
BD - Bangladesh 9
TR - Turchia 8
AE - Emirati Arabi Uniti 6
AT - Austria 6
CL - Cile 6
AU - Australia 5
MA - Marocco 5
LT - Lituania 4
LV - Lettonia 4
BG - Bulgaria 3
CO - Colombia 3
DO - Repubblica Dominicana 3
EU - Europa 3
PK - Pakistan 3
PT - Portogallo 3
TG - Togo 3
UZ - Uzbekistan 3
A2 - ???statistics.table.value.countryCode.A2??? 2
BJ - Benin 2
CH - Svizzera 2
DZ - Algeria 2
GR - Grecia 2
JM - Giamaica 2
JO - Giordania 2
RW - Ruanda 2
SA - Arabia Saudita 2
TN - Tunisia 2
VE - Venezuela 2
AM - Armenia 1
AZ - Azerbaigian 1
BA - Bosnia-Erzegovina 1
BH - Bahrain 1
BO - Bolivia 1
CD - Congo 1
CG - Congo 1
CR - Costa Rica 1
CU - Cuba 1
EG - Egitto 1
ET - Etiopia 1
GF - Guiana Francese 1
GL - Groenlandia 1
GN - Guinea 1
GY - Guiana 1
HN - Honduras 1
IR - Iran 1
KG - Kirghizistan 1
LU - Lussemburgo 1
LY - Libia 1
MK - Macedonia 1
MY - Malesia 1
NG - Nigeria 1
NP - Nepal 1
PA - Panama 1
PE - Perù 1
PS - Palestinian Territory 1
PY - Paraguay 1
RO - Romania 1
SI - Slovenia 1
SK - Slovacchia (Repubblica Slovacca) 1
SV - El Salvador 1
TH - Thailandia 1
TT - Trinidad e Tobago 1
UY - Uruguay 1
XK - ???statistics.table.value.countryCode.XK??? 1
Totale 8.738
Città #
Southend 665
Dallas 470
Chandler 384
Moscow 374
Jacksonville 255
Singapore 242
Ann Arbor 206
Hong Kong 201
Ashburn 190
Beijing 190
Woodbridge 172
Dublin 139
Verona 128
Houston 126
Jinan 86
Shenyang 77
New York 73
Wilmington 70
Nanjing 63
Lawrence 58
Princeton 58
Los Angeles 55
The Dalles 53
Ho Chi Minh City 51
Redmond 43
Tianjin 41
Columbus 40
Hebei 39
Ningbo 33
Changsha 32
Munich 32
São Paulo 31
Helsinki 30
Buffalo 29
Hanoi 28
Tokyo 27
Seattle 25
Zhengzhou 24
Nanchang 23
Haikou 22
Seoul 22
Hangzhou 21
Lanzhou 21
Warsaw 21
Brussels 20
Falls Church 20
Santa Clara 19
Redondo Beach 18
Guangzhou 17
Redwood City 17
Taiyuan 17
Jakarta 15
Taizhou 15
Boston 14
Lancaster 13
Montreal 13
San Francisco 13
Toronto 13
Dong Ket 12
Jiaxing 12
Kent 12
Milan 12
Rio de Janeiro 12
Rome 12
Belo Horizonte 11
Boardman 11
Denver 11
London 11
Sindelfingen 11
Brooklyn 10
Council Bluffs 10
Frankfurt am Main 10
Fuzhou 9
Turku 9
Dearborn 8
Elora 8
Johannesburg 8
Perugia 8
Amsterdam 7
Chennai 7
Chicago 7
Mexico City 7
Norwalk 7
Birmingham 6
Curitiba 6
Falkenstein 6
Haiphong 6
Kemerovo 6
Parma 6
Quito 6
Atlanta 5
Betim 5
Manaus 5
Orem 5
Stockholm 5
Auburn Hills 4
Brasília 4
Cagliari 4
Can Tho 4
Dongguan 4
Totale 5.523
Nome #
Analisi cinetiche, spettrofotometriche e mutazionali di due enzimi PLP-dipendenti del fold type I. Meccanismi catalitici, processi di folding e dimerizzazione 276
Gly161 mutations associated with Primary Hyperoxaluria Type I induce the cytosolic aggregation and the intracellular degradation of the apo-form of alanine:glyoxylate aminotransferase 249
Dimerization and Folding Processes of Treponema denticola Cystalysin: The Role of Pyridoxal 5'-Phosphate 232
Biochemical and computational approaches to improve the clinical treatment of Dopa decarboxylase-related diseases: an overview 230
Holo-and apocystalysin from Treponema denticola: two different conformations 229
A comprehensive picture of the mutations associated with aromatic amino acid decarboxylase deficiency: from molecular mechanisms to therapy implications 195
The novel R347g pathogenic mutation Of aromatic amino acid decarboxylase provides additional molecular insights into enzyme catalysis and deficiency 185
S250F variant associated with aromatic amino acid decarboxylase deficiency: molecular defects and intracellular rescue by pyridoxine 184
Human wild-type alanine:glyoxylate aminotransferase and its naturally occurring G82E variant: functional properties and physiological implications 176
Misfolding caused by the pathogenic mutation G47R on the minor allele of alanine:glyoxylate aminotransferase and chaperoning activity of pyridoxine 175
Effects of interface mutations on the dimerization of alanine glyoxylate aminotransferase and implications in the mistargeting of the pathogenic variants F152I and I244T 174
Biochemical analyses are instrumental in identifying the impact of mutations on holo and/or apo-forms and on the region(s) of alanine:glyoxylate aminotransferase variants associated with Primary Hyperoxaluria Type I. 171
Construction, purification and characterization of untagged human liver alanine-glyoxylate aminotransferase expressed in Escherichia coli 170
Interaction of Human Dopa Decarboxylase with L-Dopa: Spectroscopic and Kinetic Studies as a Function of pH 164
Pathogenic variants of human Aromatic L-Amino Acid Decarboxylase: evidences of misfolding in functionally active variants 163
Caenorhabditis elegans AGXT-1 is a mitochondrial and temperature-adapted ortholog of peroxisomal human AGT1: New insights into between-species divergence in glyoxylate metabolism 162
An engineered folded PLP-bound monomer of Treponema denticola cystalysin reveals the effect of the dimeric structure on the catalytic properties of the enzyme 160
Human liver peroxisomal alanine:glyoxylate aminotransferase: Characterization of the two allelic forms and their pathogenic variants. 159
Human liver peroxisomal alanine:glyoxylate aminotransferase: Different stability under chemical stress of the major allele, the minor allele, and its pathogenic G170R variant. 156
Cystalysin: an example of the catalytic versatility of pyridoxal 5'-phosphate dependent enzymes 154
Liver peroxisomal alanine:glyoxylate aminotransferase and the effects of mutations associated with Primary Hyperoxaluria Type I: An overview. 150
Tat-mediated delivery of human alanine:glyoxylate aminotransferase in a cellular model of Primary Hyperoxaluria Type I 145
The Chaperoning Activity of Amino-oxyacetic Acid on Folding-Defective Variants of Human Alanine:Glyoxylate Aminotransferase Causing Primary Hyperoxaluria Type I 144
Molecular insight into the synergism between the minor allele of human liver peroxisomal alanine: glyoxylate aminotransferase and the f152i mutation 142
New variants of AADC deficiency expand the knowledge of enzymatic phenotypes 142
Onconase Dimerization Through 3D Domain Swapping: Structural Investigations and Increase Of The Apoptotic Effect In Cancer Cells 141
Cysteine 180 Is a Redox Sensor Modulating the Activity of Human Pyridoxal 5'-Phosphate Histidine Decarboxylase 140
Molecular defects of the glycine 41 variants of alanine glyoxylate aminotransferase associated with primary hyperoxaluria type I 138
Molecular insight into the synergism between the minor allele of human liver peroxisomal alanine: Glyoxylate aminotransferase and the F152I mutation 136
The N-terminal extension is essential for the formation of the active dimeric structure of liver peroxisomal alanine:glyoxylate aminotransferase 134
Aromatic amino acid decarboxylase deficiency: Molecular and metabolic basis and therapeutic outlook 134
Deciphering the fate of slan+ -monocytes in human tonsils by gene expression profiling 133
Aromatic amino acid decarboxylase deficiency: the added value of biochemistry 133
Identification by Virtual Screening and In Vitro Testing of Human DOPA Decarboxylase Inhibitors 133
Properties of RNase A monomer and dimers depend on the oligomerization pathway followed. 132
Deficit of human ornithine aminotransferase in gyrate atrophy: Molecular, cellular, and clinical aspects 132
S81 L and G170R mutations causing Primary Hyperoxaluria Type I in homozygosis and heterozygosis: an example of positive interallelic complementation. 131
Radiation damage at the active site of human alanine:glyoxylate aminotransferase reveals that the cofactor position is finely tuned during catalysis 131
RNase A domain-swapped dimers produced through different methods: structure–catalytic properties and antitumor activity 131
Compound heterozygosis in AADC deficiency: A complex phenotype dissected through comparison among heterodimeric and homodimeric AADC proteins 131
Dimerization of human angiogenin and of variants involved in neurodegenerative diseases 127
Extensive deamidation of RNase A inhibits its oligomerization through 3D domain swapping 125
Natural and unnatural compounds rescue folding defects of human alanine:glyoxylate aminotransferase leading to Primary Hyperoxaluria Type I 122
Molecular and cellular studies reveal folding defects of human ornithine aminotransferase variants associated with gyrate atrophy of the choroid and retina 121
Evidence for dimer/tetramer equilibrium in Trypanosoma brucei 6-phosphogluconate dehydrogenase 120
The chaperone role of the pyridoxal 5′-phosphate and its implications for rare diseases involving B6-dependent enzymes 120
Oligomeric state and thermal stability of apo- and holo- human ornithine δ-aminotransferase 119
Insights into the mechanism of oxidative deamination catalyzed by Dopa decarboxylase 115
Probing the role of Tyr 64 of Treponema denticola cystalysin by site-directed mutagenesis and kinetic studies 114
R180T variant of δ-ornithine aminotransferase associated with gyrate atrophy: biochemical, computational, X-RAY and NMR studies provide insight into its catalytic features 113
A novel compound heterozygous genotype associated with aromatic amino acid decarboxylase deficiency: Clinical aspects and biochemical studies 113
Open conformation of human DOPA decarboxylase reveals the mechanism of PLP addition to Group II decarboxylases. 110
Heterozygosis in aromatic amino acid decarboxylase deficiency: Evidence for a positive interallelic complementation between R347Q and R358H mutations 107
Molecular insights into the pathogenicity of variants associated with the aromatic amino acid decarboxylase deficiency. 105
Parkinson's Disease: recent updates in the identification of human dopa decarboxylase inhibitors 105
Molecular and cellular basis of ornithine δ-aminotransferase deficiency caused by the V332M mutation associated with gyrate atrophy of the choroid and retina 101
Reactions of human liver peroxisomal alanine:glyoxylate aminotransferase with beta-chloro-L-alanine and L-cysteine: spectroscopic and kinetic analysis 100
Biochemical and bioinformatic studies of mutations of residues at the monomer-monomer interface of human ornithine aminotransferase leading to gyrate atrophy of choroid and retina 98
Biochemical investigation of pathogenic missense mutations of human 4-amino butyrate aminotransferase towards the understanding of the molecular pathogenesis of GABA transaminase deficiency 97
Molecular insights into primary hyperoxaluria Type I pathogenesis. 97
Human RNase 1 can extensively oligomerize through 3D domain swapping thanks to the crucial contribution of its C-terminus 58
Spectrum of DDC variants causing aromatic l-amino acid decarboxylase (AADC) deficiency and pathogenicity interpretation using ACMG-AMP/ACGS recommendations 48
Totale 8.832
Categoria #
all - tutte 28.807
article - articoli 26.566
book - libri 0
conference - conferenze 1.230
curatela - curatele 0
other - altro 587
patent - brevetti 0
selected - selezionate 0
volume - volumi 424
Totale 57.614


Totale Lug Ago Sett Ott Nov Dic Gen Feb Mar Apr Mag Giu
2020/2021295 0 0 0 0 79 50 9 37 24 19 52 25
2021/2022716 51 242 116 29 25 11 10 36 22 21 34 119
2022/20231.071 76 131 87 191 93 243 20 53 122 6 29 20
2023/2024489 21 40 37 60 40 92 16 45 3 23 89 23
2024/20251.518 77 84 30 240 75 55 108 68 251 138 129 263
2025/20262.628 310 200 532 606 980 0 0 0 0 0 0 0
Totale 8.832