MONTIOLI, Riccardo
 Distribuzione geografica
Continente #
NA - Nord America 4.629
EU - Europa 3.378
AS - Asia 2.910
SA - Sud America 396
Continente sconosciuto - Info sul continente non disponibili 103
AF - Africa 61
OC - Oceania 7
Totale 11.484
Nazione #
US - Stati Uniti d'America 4.510
RU - Federazione Russa 1.254
CN - Cina 1.094
SG - Singapore 988
GB - Regno Unito 761
IT - Italia 406
BR - Brasile 325
VN - Vietnam 294
HK - Hong Kong 220
SE - Svezia 181
DE - Germania 166
FR - Francia 166
IE - Irlanda 141
FI - Finlandia 119
KR - Corea 81
CA - Canada 71
BD - Bangladesh 49
UA - Ucraina 47
JP - Giappone 36
IN - India 30
PL - Polonia 27
NL - Olanda 24
ID - Indonesia 23
BE - Belgio 22
IQ - Iraq 21
AR - Argentina 20
MX - Messico 18
NG - Nigeria 17
EC - Ecuador 14
ZA - Sudafrica 14
ES - Italia 13
TR - Turchia 13
IL - Israele 12
AT - Austria 9
VE - Venezuela 9
AE - Emirati Arabi Uniti 8
CL - Cile 8
PK - Pakistan 8
UZ - Uzbekistan 8
AU - Australia 7
MA - Marocco 7
CR - Costa Rica 6
JM - Giamaica 6
LT - Lituania 6
CO - Colombia 5
JO - Giordania 5
MY - Malesia 5
PT - Portogallo 5
SA - Arabia Saudita 5
BO - Bolivia 4
CH - Svizzera 4
GR - Grecia 4
LV - Lettonia 4
TN - Tunisia 4
UY - Uruguay 4
BG - Bulgaria 3
DO - Repubblica Dominicana 3
EE - Estonia 3
EU - Europa 3
HN - Honduras 3
PY - Paraguay 3
SV - El Salvador 3
TG - Togo 3
A2 - ???statistics.table.value.countryCode.A2??? 2
AZ - Azerbaigian 2
BJ - Benin 2
DZ - Algeria 2
EG - Egitto 2
ET - Etiopia 2
MD - Moldavia 2
NI - Nicaragua 2
PE - Perù 2
PR - Porto Rico 2
RO - Romania 2
RW - Ruanda 2
AM - Armenia 1
BA - Bosnia-Erzegovina 1
BB - Barbados 1
BH - Bahrain 1
BY - Bielorussia 1
CD - Congo 1
CG - Congo 1
CI - Costa d'Avorio 1
CU - Cuba 1
GF - Guiana Francese 1
GL - Groenlandia 1
GN - Guinea 1
GY - Guiana 1
HR - Croazia 1
IR - Iran 1
KE - Kenya 1
KG - Kirghizistan 1
KW - Kuwait 1
LU - Lussemburgo 1
LY - Libia 1
MK - Macedonia 1
NO - Norvegia 1
NP - Nepal 1
PA - Panama 1
PS - Palestinian Territory 1
Totale 11.381
Città #
Southend 665
Ashburn 565
Singapore 496
Dallas 485
San Jose 449
Moscow 423
Chandler 384
Jacksonville 256
Hong Kong 218
Ann Arbor 207
Beijing 198
Verona 191
Woodbridge 172
Council Bluffs 149
Dublin 140
Houston 128
The Dalles 120
Ho Chi Minh City 109
New York 88
Jinan 86
Shenyang 77
Los Angeles 71
Wilmington 70
Hanoi 66
Nanjing 63
Lawrence 58
Princeton 58
Santa Clara 52
Redmond 43
Tianjin 42
Columbus 41
Hebei 39
Buffalo 34
Ningbo 33
São Paulo 33
Changsha 32
Helsinki 32
Munich 32
Tokyo 32
Seattle 28
Zhengzhou 25
Nanchang 23
Seoul 23
Warsaw 23
Haikou 22
Hangzhou 22
Lanzhou 21
Brussels 20
Denver 20
Falls Church 20
Milan 20
Montreal 19
Toronto 19
Guangzhou 18
Orem 18
Redondo Beach 18
Redwood City 17
Taiyuan 17
Boston 16
Frankfurt am Main 16
Jakarta 16
Brooklyn 15
Taizhou 15
Abuja 14
Atlanta 14
Chennai 14
London 14
Rome 14
San Francisco 14
Lancaster 13
Belo Horizonte 12
Chicago 12
Dong Ket 12
Jiaxing 12
Kent 12
Rio de Janeiro 12
Amsterdam 11
Boardman 11
Las Vegas 11
Sindelfingen 11
Haiphong 10
Mexico City 10
Dearborn 9
Fuzhou 9
Johannesburg 9
Phoenix 9
Turku 9
Da Nang 8
Elora 8
Perugia 8
Stockholm 8
Tashkent 8
Can Tho 7
Norwalk 7
Birmingham 6
Brescia 6
Curitiba 6
Falkenstein 6
Kemerovo 6
Parma 6
Totale 7.276
Nome #
Analisi cinetiche, spettrofotometriche e mutazionali di due enzimi PLP-dipendenti del fold type I. Meccanismi catalitici, processi di folding e dimerizzazione 352
Gly161 mutations associated with Primary Hyperoxaluria Type I induce the cytosolic aggregation and the intracellular degradation of the apo-form of alanine:glyoxylate aminotransferase 319
Dimerization and Folding Processes of Treponema denticola Cystalysin: The Role of Pyridoxal 5'-Phosphate 299
Holo-and apocystalysin from Treponema denticola: two different conformations 284
Biochemical and computational approaches to improve the clinical treatment of Dopa decarboxylase-related diseases: an overview 271
A comprehensive picture of the mutations associated with aromatic amino acid decarboxylase deficiency: from molecular mechanisms to therapy implications 243
Human wild-type alanine:glyoxylate aminotransferase and its naturally occurring G82E variant: functional properties and physiological implications 241
Pathogenic variants of human Aromatic L-Amino Acid Decarboxylase: evidences of misfolding in functionally active variants 238
S250F variant associated with aromatic amino acid decarboxylase deficiency: molecular defects and intracellular rescue by pyridoxine 230
Effects of interface mutations on the dimerization of alanine glyoxylate aminotransferase and implications in the mistargeting of the pathogenic variants F152I and I244T 222
The novel R347g pathogenic mutation Of aromatic amino acid decarboxylase provides additional molecular insights into enzyme catalysis and deficiency 221
Misfolding caused by the pathogenic mutation G47R on the minor allele of alanine:glyoxylate aminotransferase and chaperoning activity of pyridoxine 214
An engineered folded PLP-bound monomer of Treponema denticola cystalysin reveals the effect of the dimeric structure on the catalytic properties of the enzyme 210
Construction, purification and characterization of untagged human liver alanine-glyoxylate aminotransferase expressed in Escherichia coli 209
Biochemical analyses are instrumental in identifying the impact of mutations on holo and/or apo-forms and on the region(s) of alanine:glyoxylate aminotransferase variants associated with Primary Hyperoxaluria Type I. 209
Caenorhabditis elegans AGXT-1 is a mitochondrial and temperature-adapted ortholog of peroxisomal human AGT1: New insights into between-species divergence in glyoxylate metabolism 205
Human liver peroxisomal alanine:glyoxylate aminotransferase: Different stability under chemical stress of the major allele, the minor allele, and its pathogenic G170R variant. 204
Oligomeric state and thermal stability of apo- and holo- human ornithine δ-aminotransferase 203
Interaction of Human Dopa Decarboxylase with L-Dopa: Spectroscopic and Kinetic Studies as a Function of pH 201
Human liver peroxisomal alanine:glyoxylate aminotransferase: Characterization of the two allelic forms and their pathogenic variants. 199
Cysteine 180 Is a Redox Sensor Modulating the Activity of Human Pyridoxal 5'-Phosphate Histidine Decarboxylase 193
New variants of AADC deficiency expand the knowledge of enzymatic phenotypes 190
Liver peroxisomal alanine:glyoxylate aminotransferase and the effects of mutations associated with Primary Hyperoxaluria Type I: An overview. 189
Cystalysin: an example of the catalytic versatility of pyridoxal 5'-phosphate dependent enzymes 187
The N-terminal extension is essential for the formation of the active dimeric structure of liver peroxisomal alanine:glyoxylate aminotransferase 186
Onconase Dimerization Through 3D Domain Swapping: Structural Investigations and Increase Of The Apoptotic Effect In Cancer Cells 182
Molecular insight into the synergism between the minor allele of human liver peroxisomal alanine: Glyoxylate aminotransferase and the F152I mutation 180
Dimerization of human angiogenin and of variants involved in neurodegenerative diseases 177
Tat-mediated delivery of human alanine:glyoxylate aminotransferase in a cellular model of Primary Hyperoxaluria Type I 176
S81 L and G170R mutations causing Primary Hyperoxaluria Type I in homozygosis and heterozygosis: an example of positive interallelic complementation. 176
The Chaperoning Activity of Amino-oxyacetic Acid on Folding-Defective Variants of Human Alanine:Glyoxylate Aminotransferase Causing Primary Hyperoxaluria Type I 176
Deciphering the fate of slan+ -monocytes in human tonsils by gene expression profiling 176
Aromatic amino acid decarboxylase deficiency: the added value of biochemistry 171
Aromatic amino acid decarboxylase deficiency: Molecular and metabolic basis and therapeutic outlook 170
RNase A domain-swapped dimers produced through different methods: structure–catalytic properties and antitumor activity 169
Molecular and cellular studies reveal folding defects of human ornithine aminotransferase variants associated with gyrate atrophy of the choroid and retina 168
Molecular insight into the synergism between the minor allele of human liver peroxisomal alanine: glyoxylate aminotransferase and the f152i mutation 166
R180T variant of δ-ornithine aminotransferase associated with gyrate atrophy: biochemical, computational, X-RAY and NMR studies provide insight into its catalytic features 166
Natural and unnatural compounds rescue folding defects of human alanine:glyoxylate aminotransferase leading to Primary Hyperoxaluria Type I 165
Deficit of human ornithine aminotransferase in gyrate atrophy: Molecular, cellular, and clinical aspects 164
Properties of RNase A monomer and dimers depend on the oligomerization pathway followed. 163
Identification by Virtual Screening and In Vitro Testing of Human DOPA Decarboxylase Inhibitors 163
Molecular defects of the glycine 41 variants of alanine glyoxylate aminotransferase associated with primary hyperoxaluria type I 162
Compound heterozygosis in AADC deficiency: A complex phenotype dissected through comparison among heterodimeric and homodimeric AADC proteins 161
Molecular and cellular basis of ornithine δ-aminotransferase deficiency caused by the V332M mutation associated with gyrate atrophy of the choroid and retina 160
The chaperone role of the pyridoxal 5′-phosphate and its implications for rare diseases involving B6-dependent enzymes 158
Evidence for dimer/tetramer equilibrium in Trypanosoma brucei 6-phosphogluconate dehydrogenase 156
Radiation damage at the active site of human alanine:glyoxylate aminotransferase reveals that the cofactor position is finely tuned during catalysis 155
Biochemical and bioinformatic studies of mutations of residues at the monomer-monomer interface of human ornithine aminotransferase leading to gyrate atrophy of choroid and retina 152
Extensive deamidation of RNase A inhibits its oligomerization through 3D domain swapping 152
A novel compound heterozygous genotype associated with aromatic amino acid decarboxylase deficiency: Clinical aspects and biochemical studies 151
Insights into the mechanism of oxidative deamination catalyzed by Dopa decarboxylase 147
Heterozygosis in aromatic amino acid decarboxylase deficiency: Evidence for a positive interallelic complementation between R347Q and R358H mutations 145
Parkinson's Disease: recent updates in the identification of human dopa decarboxylase inhibitors 140
Open conformation of human DOPA decarboxylase reveals the mechanism of PLP addition to Group II decarboxylases. 139
Probing the role of Tyr 64 of Treponema denticola cystalysin by site-directed mutagenesis and kinetic studies 136
Biochemical investigation of pathogenic missense mutations of human 4-amino butyrate aminotransferase towards the understanding of the molecular pathogenesis of GABA transaminase deficiency 135
Molecular insights into the pathogenicity of variants associated with the aromatic amino acid decarboxylase deficiency. 132
Molecular insights into primary hyperoxaluria Type I pathogenesis. 130
Reactions of human liver peroxisomal alanine:glyoxylate aminotransferase with beta-chloro-L-alanine and L-cysteine: spectroscopic and kinetic analysis 125
Human RNase 1 can extensively oligomerize through 3D domain swapping thanks to the crucial contribution of its C-terminus 109
Spectrum of DDC variants causing aromatic l-amino acid decarboxylase (AADC) deficiency and pathogenicity interpretation using ACMG-AMP/ACGS recommendations 88
Current Insight into Human Ornithine Aminotransferase: A Review 24
Totale 11.484
Categoria #
all - tutte 37.356
article - articoli 34.476
book - libri 0
conference - conferenze 1.599
curatela - curatele 0
other - altro 744
patent - brevetti 0
selected - selezionate 0
volume - volumi 537
Totale 74.712


Totale Lug Ago Sett Ott Nov Dic Gen Feb Mar Apr Mag Giu
2021/2022307 0 0 0 29 25 11 10 36 22 21 34 119
2022/20231.071 76 131 87 191 93 243 20 53 122 6 29 20
2023/2024489 21 40 37 60 40 92 16 45 3 23 89 23
2024/20251.518 77 84 30 240 75 55 108 68 251 138 129 263
2025/20264.658 310 200 532 606 1.116 329 470 225 339 296 98 137
2026/2027622 54 103 160 305 0 0 0 0 0 0 0 0
Totale 11.484