INTRODUCTION: Perivascular epithelioid cell tumors (PEComa) are a very uncommon mesenchymal cancer with uncertain malignant potential.MATERIALS AND METHODS: A computerized research on Pub Med was performed regarding bladder PEComa. We evaluated the literature cases and described a case of bladder PEComa.RESULTS: PEComa of the bladder is a very rare neoplasm and only 15 cases have been reported so far.CONCLUSION: Bladder PEComa involves young subjects of both genders, mostly under 40 years of age. Surgical treatment (partial or radical cystectomy) is the most common management.A long-term follow-up and larger series are required to better understand the best clinical approach to bladder PEComa.
Bladder perivascular epithelioid cell tumor (PEComa): a case report and literature review
CERRUTO, Maria Angela;BRUNELLI, Matteo;
2015-01-01
Abstract
INTRODUCTION: Perivascular epithelioid cell tumors (PEComa) are a very uncommon mesenchymal cancer with uncertain malignant potential.MATERIALS AND METHODS: A computerized research on Pub Med was performed regarding bladder PEComa. We evaluated the literature cases and described a case of bladder PEComa.RESULTS: PEComa of the bladder is a very rare neoplasm and only 15 cases have been reported so far.CONCLUSION: Bladder PEComa involves young subjects of both genders, mostly under 40 years of age. Surgical treatment (partial or radical cystectomy) is the most common management.A long-term follow-up and larger series are required to better understand the best clinical approach to bladder PEComa.
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