Paroxysmal dysarthria-ataxia is a rare neurological condition due to ephaptic transmission, generally appearing in multiple sclerosis patients characterized by stereotyped attacks of slurred speech usually accompanied by ataxia, appearing many times a day. Here we describe a patient with an unusual remitting-relapsing form of Bickerstaff's-like brainstem encephalitis who manifested PDA after a relapse with the involvement of a peculiar region below the red nuclei and benefited from lamotrigine.

Paroxysmal dysarthria-ataxia in remitting-relapsing Bickerstaff's-like encephalitis.

PIFFER, SILVIO;TURRI, Giulia;ACLER, Michele;RICHELLI, Silvia;CERINI, ROBERTO;FIASCHI, Antonio;MONACO, Salvatore;BONETTI, Bruno
2014-01-01

Abstract

Paroxysmal dysarthria-ataxia is a rare neurological condition due to ephaptic transmission, generally appearing in multiple sclerosis patients characterized by stereotyped attacks of slurred speech usually accompanied by ataxia, appearing many times a day. Here we describe a patient with an unusual remitting-relapsing form of Bickerstaff's-like brainstem encephalitis who manifested PDA after a relapse with the involvement of a peculiar region below the red nuclei and benefited from lamotrigine.
2014
Bickerstaff's brainstem encephalitis; autoimmune diseases of the nervous system; brainstem dysfunction; paroxysmal dysarthria-ataxia syndrome; ephaptic axonal activation; brainstem MRI abnormalities
File in questo prodotto:
Non ci sono file associati a questo prodotto.

I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.

Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11562/717562
Citazioni
  • ???jsp.display-item.citation.pmc??? 2
  • Scopus 6
  • ???jsp.display-item.citation.isi??? 5
social impact