INTRODUCTION: Primary heart involvement (pHI) is an overlooked and poorly characterised complication of systemic sclerosis (SSc), associated with the risk of heart failure, arrhythmia and death. Despite consensus definition by the World Scleroderma Foundation/Heart Failure Association (WSF/HFA), diagnostic criteria and risk factors remain poorly elucidated.

First-line diagnostic tests to intercept primary heart involvement in systemic sclerosis: Clinical associations from the SPRING-SIR registry

Motta, Francesca;Zanatta, Elisabetta;Bosello, Silvia Laura;Idolazzi, Luca;De Lorenzis, Enrico;De Santis, Maria;
2025-01-01

Abstract

INTRODUCTION: Primary heart involvement (pHI) is an overlooked and poorly characterised complication of systemic sclerosis (SSc), associated with the risk of heart failure, arrhythmia and death. Despite consensus definition by the World Scleroderma Foundation/Heart Failure Association (WSF/HFA), diagnostic criteria and risk factors remain poorly elucidated.
2025
systemic sclerosis, pulmonary hypertension
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11562/1170170
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