Primary hemophagocytic lymphohistiocytosis is a rare syndrome characterized by immune dysregulation and hyperinflammation. It typically manifests in infancy and is associated with high mortality.

Emapalumab in Children with Primary Hemophagocytic Lymphohistiocytosis

Cesaro, Simone;
2020-01-01

Abstract

Primary hemophagocytic lymphohistiocytosis is a rare syndrome characterized by immune dysregulation and hyperinflammation. It typically manifests in infancy and is associated with high mortality.
2020
Adolescent
Age of Onset
Anti-Inflammatory Agents
Antibodies, Monoclonal
Antibodies, Neutralizing
Chemokine CXCL9
Child
Child, Preschool
Dexamethasone
Drug Therapy, Combination
Female
Hematopoietic Stem Cell Transplantation
Humans
Infant
Infections
Interferon-gamma
Kaplan-Meier Estimate
Lymphohistiocytosis, Hemophagocytic
Male
Treatment Outcome
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11562/1033422
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