Mayer-Rokitansky-Küster-Hauser syndrome (MRKH syndrome) is characterized by Müllerian duct structures agenesis: the vagina atresia is the commonest variant. There can be some anomalies associated, such as renal, skeletal, spine malformations and others. Patients with MRKH can show different presentation from newborn period to adolescence. We report our experience in treatment of the vaginal atresia presenting in two young girls as a sign of MRKH syndrome.

Mayer-Rokitansky-Küster-Hauser syndrome presenting as vaginal atresia: report of two cases

Pedrazzani, C;
2008-01-01

Abstract

Mayer-Rokitansky-Küster-Hauser syndrome (MRKH syndrome) is characterized by Müllerian duct structures agenesis: the vagina atresia is the commonest variant. There can be some anomalies associated, such as renal, skeletal, spine malformations and others. Patients with MRKH can show different presentation from newborn period to adolescence. We report our experience in treatment of the vaginal atresia presenting in two young girls as a sign of MRKH syndrome.
Abnormalities, Multiple
Adolescent
Adult
Amenorrhea
Diagnosis, Differential
Female
Gonadal Dysgenesis
Humans
Mullerian Ducts
Syndrome
Treatment Outcome
Uterus
Vagina
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11562/1029775
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