Sfoglia per Autore
Pharmacological Inhibition of Calpain-1 Prevents Red Cell Dehydration and Reduces Gardos Channel Activity in a Mouse Model of Sickle Cell Disease. Identification of Druggable Protease Target
2011-01-01 De Franceschi, Lucia; Matte, Alessandro; Brugnara, Carlo; Siciliano, Angela; Bertoldi, Mariarita; Wieschhaus, Adam; Chishti, Athar H.
Erythrocyte membrane changes of chorea-acanthocytosis are the result of altered Lyn kinase activity
2011-01-01 DE FRANCESCHI, Lucia; Tomelleri, Carlo; Matte', Alessandro; Brunati, Am; Bovee Geurts, Ph; Bertoldi, Mariarita; Lasonder, E; Tibaldi, E; Danek, A; Walker, Rh; Jung, Hh; Bader, B; Siciliano, Angela; Ferru, E; Mohandas, N; Bosman, Gjcgm
Oxidative stress modulates heme synthesis and induces peroxiredoxin-2 as a novel cytoprotective response in β-thalassemic erythropoiesis
2011-01-01 DE FRANCESCHI, Lucia; Bertoldi, Mariarita; De Falco, L; SANTOS FRANCO, Sara; Ronzoni, L; Turrini, F; Colancecco, A; Camaschella, C; Cappellini, Md; Iolascon, A.
Does the aromatic L-amino acid decarboxylase contribute to thyronamine biosynthesis?
2012-01-01 Hoefig, C. S.; Renko, K.; Piehl, S.; Scanlan, T. S.; Bertoldi, Mariarita; Opladen, T.; Hoffman, G. F.; Klein, J.; Blankenstein, O.; Schweizer, U.; Koehrle, J.
Resveratrol Induces Erythroid Maturation by Activating FOXO3 and Improves in Vivo Erythropoiesis in Normal and Beta -Thalassemic Mice
2013-01-01 SANTOS FRANCO, Sara; Luigia De, Falco; Saghi, Ghaffari; Carlo, Brugnara; David, Sinclair; Achille, Iolascon; Mohandas, Narla; Bertoldi, Mariarita; Christophe, Lebouf; Anne, Janin; Siciliano, Angela; Pauline, Rimmele; Maria Domenica, Cappellini; Shady, Michan; Zoratti, Elisa; DE FRANCESCHI, Lucia
Oxidative stress and b-thalasssemic erythroid cells behind the molecular defect
2013-01-01 DE FRANCESCHI, Lucia; Bertoldi, Mariarita; Matte', Alessandro; SANTOS FRANCO, Sara; Pantaleo, A; Ferru, E; Turrini, F.
Pharmacological inhibition of calpain-1 prevents red cell dehydration and reduces Gardos channel activity in a mouse model of sickle cell disease
2013-01-01 DE FRANCESCHI, Lucia; Franco, R. S.; Bertoldi, Mariarita; Brugnara, C.; Matte', Alessandro; Siciliano, Angela; Wieschhaus, A. J.; Chishti, A. H.; Joiner, C. H.
Membrane association of peroxiredoxin-2 in red cells is mediated by the N-terminal cytoplasmic domain of band3
2013-01-01 Matte', Alessandro; Bertoldi, Mariarita; Mohandas, N; An, X; Bugatti, A; Brunati, Am; Rusnati, M; Tibaldi, E; Siciliano, Angela; Turrini, F; Perrotta, S; DE FRANCESCHI, Lucia
Resveratrol accelerates erythroid maturation by activation of FoxO3 and ameliorates anemia in beta-thalassemic mice
2014-01-01 SANTOS FRANCO, Sara; De Falco, L; Ghaffari, S; Brugnara, C; Sinclair, Da; Matte', Alessandro; Iolascon, A; Mohandas, N; Bertoldi, Mariarita; An, X; Siciliano, Angela; Rimelle, P; Cappellini, Md; Michan, S; Zoratti, E; Janin, A; DE FRANCESCHI, Lucia
Mammalian Dopa decarboxylase: structure, catalytic activity and inhibition
2014-01-01 Bertoldi, Mariarita
The novel role of peroxiredoxin-2 in red cell membrane protein homeostasis and senescence.
2014-01-01 Matte', Alessandro; Pantaleo, A; Ferru, E; Turrini, F; Bertoldi, Mariarita; Lupo, Francesca; Siciliano, Angela; Ho Zoon, C; DE FRANCESCHI, Lucia
The novel R347g pathogenic mutation Of aromatic amino acid decarboxylase provides additional molecular insights into enzyme catalysis and deficiency
2016-01-01 Montioli, Riccardo; Paiardini, Alessandro; Kurian, Manju A.; Dindo, Mirco; Rossignoli, Giada; Heales, Simon J. R.; Pope, Simon; Voltattorni, Carla Borri; Bertoldi, Mariarita
A new molecular link between defective autophagy and erythroid abnormalities in chorea-acanthocytosis
2016-01-01 Lupo, Francesca; Tibaldi, Elena; Matte', Alessandro; Sharma, Alok K.; Brunati, Anna Maria; Alper, Seth L.; Zancanaro, Carlo; Benati, Donatella; Siciliano, Angela; Bertoldi, Mariarita; Zonti, Francesca; Storch, Alexander; Walker, Ruth H.; Danek, Adrian; Bader, Benedikt; Hermann, Andreas; DE FRANCESCHI, Lucia
Parkinson's Disease: recent updates in the identification of human dopa decarboxylase inhibitors
2016-01-01 Montioli, Riccardo; Voltattorni, Carla B; Bertoldi, Mariarita
Human peroxiredoxins 1 and 2 and their interacting protein partners; through structure toward functions of biological complexes
2016-01-01 Bertoldi, Mariarita
Unique substrate specificity of ornithine aminotransferase from Toxoplasma gondii
2017-01-01 Astegno, Alessandra; Maresi, Elena; Bertoldi, Mariarita; LA VERDE, Valentina; Paiardini, Alessandro; Dominici, Paola
New insights emerging from recent investigations on human group II pyridoxal 5'-phosphate Decarboxylases
2017-01-01 Paiardini, Alessandro; Giardina, Giorgio; Rossignoli, Giada; Voltattorni, Carla Borri; Bertoldi, Mariarita
Pathogenic variants of human Aromatic L-Amino Acid Decarboxylase: evidences of misfolding in functionally active variants
2018-01-01 Bisello, Giovanni; Montioli, Riccardo; Dindo, Mirco; Voltattorni Carla, Borri; Bertoldi, Mariarita
Heterozygosis in aromatic amino acid decarboxylase deficiency: Evidence for a positive interallelic complementation between R347Q and R358H mutations
2018-01-01 Montioli, Riccardo; Janson, Giacomo; Paiardini, Alessandro; Bertoldi, Mariarita; Borri Voltattorni, Carla
Phosphorylation of pyridoxal 5'-phosphate enzymes: an intriguing and neglected topic
2018-01-01 Rossignoli, Giada; Phillips, Robert S; Astegno, Alessandra; Menegazzi, Marta; Voltattorni, Carla Borri; Bertoldi, Mariarita
Titolo | Data di pubblicazione | Autore(i) | File |
---|---|---|---|
Pharmacological Inhibition of Calpain-1 Prevents Red Cell Dehydration and Reduces Gardos Channel Activity in a Mouse Model of Sickle Cell Disease. Identification of Druggable Protease Target | 1-gen-2011 | De Franceschi, Lucia; Matte, Alessandro; Brugnara, Carlo; Siciliano, Angela; Bertoldi, Mariarita; Wieschhaus, Adam; Chishti, Athar H. | |
Erythrocyte membrane changes of chorea-acanthocytosis are the result of altered Lyn kinase activity | 1-gen-2011 | DE FRANCESCHI, Lucia; Tomelleri, Carlo; Matte', Alessandro; Brunati, Am; Bovee Geurts, Ph; Bertoldi, Mariarita; Lasonder, E; Tibaldi, E; Danek, A; Walker, Rh; Jung, Hh; Bader, B; Siciliano, Angela; Ferru, E; Mohandas, N; Bosman, Gjcgm | |
Oxidative stress modulates heme synthesis and induces peroxiredoxin-2 as a novel cytoprotective response in β-thalassemic erythropoiesis | 1-gen-2011 | DE FRANCESCHI, Lucia; Bertoldi, Mariarita; De Falco, L; SANTOS FRANCO, Sara; Ronzoni, L; Turrini, F; Colancecco, A; Camaschella, C; Cappellini, Md; Iolascon, A. | |
Does the aromatic L-amino acid decarboxylase contribute to thyronamine biosynthesis? | 1-gen-2012 | Hoefig, C. S.; Renko, K.; Piehl, S.; Scanlan, T. S.; Bertoldi, Mariarita; Opladen, T.; Hoffman, G. F.; Klein, J.; Blankenstein, O.; Schweizer, U.; Koehrle, J. | |
Resveratrol Induces Erythroid Maturation by Activating FOXO3 and Improves in Vivo Erythropoiesis in Normal and Beta -Thalassemic Mice | 1-gen-2013 | SANTOS FRANCO, Sara; Luigia De, Falco; Saghi, Ghaffari; Carlo, Brugnara; David, Sinclair; Achille, Iolascon; Mohandas, Narla; Bertoldi, Mariarita; Christophe, Lebouf; Anne, Janin; Siciliano, Angela; Pauline, Rimmele; Maria Domenica, Cappellini; Shady, Michan; Zoratti, Elisa; DE FRANCESCHI, Lucia | |
Oxidative stress and b-thalasssemic erythroid cells behind the molecular defect | 1-gen-2013 | DE FRANCESCHI, Lucia; Bertoldi, Mariarita; Matte', Alessandro; SANTOS FRANCO, Sara; Pantaleo, A; Ferru, E; Turrini, F. | |
Pharmacological inhibition of calpain-1 prevents red cell dehydration and reduces Gardos channel activity in a mouse model of sickle cell disease | 1-gen-2013 | DE FRANCESCHI, Lucia; Franco, R. S.; Bertoldi, Mariarita; Brugnara, C.; Matte', Alessandro; Siciliano, Angela; Wieschhaus, A. J.; Chishti, A. H.; Joiner, C. H. | |
Membrane association of peroxiredoxin-2 in red cells is mediated by the N-terminal cytoplasmic domain of band3 | 1-gen-2013 | Matte', Alessandro; Bertoldi, Mariarita; Mohandas, N; An, X; Bugatti, A; Brunati, Am; Rusnati, M; Tibaldi, E; Siciliano, Angela; Turrini, F; Perrotta, S; DE FRANCESCHI, Lucia | |
Resveratrol accelerates erythroid maturation by activation of FoxO3 and ameliorates anemia in beta-thalassemic mice | 1-gen-2014 | SANTOS FRANCO, Sara; De Falco, L; Ghaffari, S; Brugnara, C; Sinclair, Da; Matte', Alessandro; Iolascon, A; Mohandas, N; Bertoldi, Mariarita; An, X; Siciliano, Angela; Rimelle, P; Cappellini, Md; Michan, S; Zoratti, E; Janin, A; DE FRANCESCHI, Lucia | |
Mammalian Dopa decarboxylase: structure, catalytic activity and inhibition | 1-gen-2014 | Bertoldi, Mariarita | |
The novel role of peroxiredoxin-2 in red cell membrane protein homeostasis and senescence. | 1-gen-2014 | Matte', Alessandro; Pantaleo, A; Ferru, E; Turrini, F; Bertoldi, Mariarita; Lupo, Francesca; Siciliano, Angela; Ho Zoon, C; DE FRANCESCHI, Lucia | |
The novel R347g pathogenic mutation Of aromatic amino acid decarboxylase provides additional molecular insights into enzyme catalysis and deficiency | 1-gen-2016 | Montioli, Riccardo; Paiardini, Alessandro; Kurian, Manju A.; Dindo, Mirco; Rossignoli, Giada; Heales, Simon J. R.; Pope, Simon; Voltattorni, Carla Borri; Bertoldi, Mariarita | |
A new molecular link between defective autophagy and erythroid abnormalities in chorea-acanthocytosis | 1-gen-2016 | Lupo, Francesca; Tibaldi, Elena; Matte', Alessandro; Sharma, Alok K.; Brunati, Anna Maria; Alper, Seth L.; Zancanaro, Carlo; Benati, Donatella; Siciliano, Angela; Bertoldi, Mariarita; Zonti, Francesca; Storch, Alexander; Walker, Ruth H.; Danek, Adrian; Bader, Benedikt; Hermann, Andreas; DE FRANCESCHI, Lucia | |
Parkinson's Disease: recent updates in the identification of human dopa decarboxylase inhibitors | 1-gen-2016 | Montioli, Riccardo; Voltattorni, Carla B; Bertoldi, Mariarita | |
Human peroxiredoxins 1 and 2 and their interacting protein partners; through structure toward functions of biological complexes | 1-gen-2016 | Bertoldi, Mariarita | |
Unique substrate specificity of ornithine aminotransferase from Toxoplasma gondii | 1-gen-2017 | Astegno, Alessandra; Maresi, Elena; Bertoldi, Mariarita; LA VERDE, Valentina; Paiardini, Alessandro; Dominici, Paola | |
New insights emerging from recent investigations on human group II pyridoxal 5'-phosphate Decarboxylases | 1-gen-2017 | Paiardini, Alessandro; Giardina, Giorgio; Rossignoli, Giada; Voltattorni, Carla Borri; Bertoldi, Mariarita | |
Pathogenic variants of human Aromatic L-Amino Acid Decarboxylase: evidences of misfolding in functionally active variants | 1-gen-2018 | Bisello, Giovanni; Montioli, Riccardo; Dindo, Mirco; Voltattorni Carla, Borri; Bertoldi, Mariarita | |
Heterozygosis in aromatic amino acid decarboxylase deficiency: Evidence for a positive interallelic complementation between R347Q and R358H mutations | 1-gen-2018 | Montioli, Riccardo; Janson, Giacomo; Paiardini, Alessandro; Bertoldi, Mariarita; Borri Voltattorni, Carla | |
Phosphorylation of pyridoxal 5'-phosphate enzymes: an intriguing and neglected topic | 1-gen-2018 | Rossignoli, Giada; Phillips, Robert S; Astegno, Alessandra; Menegazzi, Marta; Voltattorni, Carla Borri; Bertoldi, Mariarita |
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